Iduronate Sulfate Sulfatase
《英文msh詞典》Iduronate Sulfate Sulfatase
[入口詞] Iduronate Sulfate Sulfatase
[主題詞] Iduronate Sulfatase
[英文釋義] An enzyme that specifically cleaves the ester sulfate of iduronic acid. Its deficiency has been demonstrated in Hunter's syndrome,which is characterized by an excess of dermatan sulfate and heparan sulfate. EC 3.1.6.13.